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DEGRADATION OF KERATAN SULPHATE BY BETA -N-ACETYLHEXOSAMINIDASES A AND BLUDOLPH T; PASCHKE E; GLOSSL J et al.1981; BIOCHEM. J. (LOND.); ISSN 0006-2936; GBR; DA. 1981; VOL. 193; NO 3; PP. 811-818; BIBL. 35 REF.Article

PINOCYTOSIS OF INTRACELLULAR AND SECRETED BETA -HEXOSAMINIDASE FROM HUMAN FIBROBLASTSKAPLAN A.1980; ARCH. BIOCHEM. BIOPHYS.; USA; DA. 1980; VOL. 202; NO 1; PP. 76-82; BIBL. 21 REF.Article

ABSENCE OF HEXOSAMINIDASE A AND B IN A NORMAL ADULT = ABSENCE D'HEXOSAMINIDASE A ET B CHEZ UN ADULTE NORMALDREYFUS JC; POENARU L; SVENNERHOLM L et al.1975; NEW ENGL. J. MED.; U.S.A.; DA. 1975; VOL. 292; NO 2; PP. 61-63; BIBL. 21REF.Article

HUMAN SS-D-N-ACETYLHEXOSAMINIDASES A AND B: EXPRESSION AND LINKAGE RELATIONSHIPS IN SOMATIC CELL HYBRIDSLALLEY PA; RATTAZZI MC; SHOWS TB et al.1974; PROC. NATION. ACAD. SCI. U.S.A.; U.S.A.; DA. 1974; VOL. 71; NO 4; PP. 1569-1573; BIBL. 38REF.Article

APPARENT HEXOSAMINIDASE B DEFIENCY IN TWO HEALTHY MEMBERS OF A PEDIGREEHECHTMAN P; ROWLANDS A.1979; AMER. J. HUM. GENET.; USA; DA. 1979; VOL. 31; NO 4; PP. 428-438; BIBL. 24 REF.Article

HIGH-CAPACITY METHOD FOR PURIFICATION OF HUMAN LIVER HEXOSAMINIDASE B USING HYDROPHOBIC CHROMATOGRAPHYHARDWICK J; HECHTMAN P.1980; J. CHROMATOGR.; NLD; DA. 1980; VOL. 190; NO 2; PP. 385-391; BIBL. 14 REF.Article

NONENZYMATIC CONVERSION OF HUMAN HEXOSAMINIDASE A.BEUTLER E; VILLACORTE D; KUHL W et al.1975; J. LAB. CLIN. MED.; U.S.A.; DA. 1975; VOL. 86; NO 2; PP. 195-203; BIBL. 17 REF.Article

ASSIGNMENT OF THE HUMAN GENE FOR HEXOSAMINIDASE B TO CHROMOSOME 5.BOEDECKER HJ; MELLMAN WJ; TEDESCO TA et al.1975; EXPER. CELL RES.; U.S.A.; DA. 1975; VOL. 93; NO 2; PP. 468-472; BIBL. 12 REF.Article

SECRETION OF BETA -HEXOSAMINIDASE BY CULTURED HUMAN SKIN FIBROBLASTS. KINETICS, EFFECT OF TEMPERATURE, CELL DENSITY, SERUM CONCENTRATION AND PH.VON FIGURA K.1978; EXPER. CELL RES.; U.S.A.; DA. 1978; VOL. 111; NO 1; PP. 15-21; BIBL. 16 REF.Article

SANDHOFF'S DISEASE (GM2 GANGLIOSIDOSIS TYPE 2). CLINICAL, CHEMICAL, AND ENZYME STUDIES IN FIVE PATIENTS = LA MALADIE DE SANDHOFF OU GANGLIOSIDOSE GM2 DE TYPE 2. ETUDES CLINIQUES, CHIMIQUES ET ENZYMATIQUES CHEZ CINQ MALADESOKADA S; MCCREA M; O'BRIEN JS et al.1972; PEDIATR. RES.; SWITZ.; DA. 1972; VOL. 6; NO 7; PP. 606-615; BIBL. 38REF.Serial Issue

ACIDE HYDROLASES AND TRYPTASE FROM SECRETORY GRANULES OF DISPERSED HUMAN LUNG MAST CELLSSCHWARTZ LB; LEWIS RA; SELDIN D et al.1981; J. IMMUNOL.; ISSN 0022-1767; USA; DA. 1981; VOL. 126; NO 4; PP. 1290-1294; BIBL. 27 REF.Article

CARBOHYDRATE COMPOSITION OF HUMAN PLACENTAL N-ACETYLHEXOSAMINIDASES A AND BFREEZE H; GEIGER B; MILLER AL et al.1979; BIOCHEM. J.; GBR; DA. 1979; VOL. 177; NO 2; PP. 749-752; BIBL. 33 REF.Article

CHARACTERIZATION OF PROTEINS STRUCTURALLY RELATED TO HUMAN N-ACETYL-BETA -D-GLUCOSAMINIDASE.CARROLL M.1978; BIOCHEM. J.; GBR; DA. 1978; VOL. 173; NO 1; PP. 191-196; BIBL. 32 REF.Article

STUDIES ON BETA -D-N-ACETYLHEXOSAMINIDASE. VARIOUS ISOZYMES IN TISSUES OF NORMAL SUBJECTS AND SANDHOFF'S DISEASE PATIENTS.SRIVASTAVA SK; WIKTOROWICZ J; KLEBE R et al.1975; BIOCHIM. BIOPHYS. ACTA; PAYS-BAS; DA. 1975; VOL. 397; NO 3; PP. 428-436; BIBL. 24 REF.Article

BETA-HEXOSAMINIDASE ACTIVITIES IN TEARS AND PLASMA DIPHOSPHOGLYCERATE IN BLOOD OF DIABETIC PATIENTS.VAN HAERINGEN NJ; VROOLAND JL; GLASIUS E et al.1978; CLIN. CHIM. ACTA; NLD; DA. 1978; VOL. 86; NO 3; PP. 333-338; BIBL. 14 REF.Article

ACTIVITY OF N-ACETYL-BETA -D-HEXOSAMINIDASES A AND B FROM HUMAN LIVER TOWARDS VARIOUS OLIGOSACCHARIDES AND A GLYCOPEPTIDE CORE DERIVED FROM GLYCOPROTEINS.BEARPARK T; BOUQUELET S; FOURNET B et al.1977; F.E.B.S. LETTERS; NETHERL.; DA. 1977; VOL. 84; NO 2; PP. 379-384; BIBL. 19 REF.Article

TAY-SACHS' AND SANDHOFF'S DISEASES: THE ASSIGNMENT OF GENES FOR HEXOSAMINIDASE A AND B TO INDIVIDUAL HUMAN CHROMOSOMESGILBERT F; KUCHERLAPATI R; CREAGAN RP et al.1975; PROC. NATION. ACAD. SCI. U.S.A.; U.S.A.; DA. 1975; VOL. 72; NO 1; PP. 263-267; BIBL. 18REF.Article

PRESENCE OF AN ATYPICAL THERMOLABILE SPECIES OF BETA -HEXOSAMINIDASE B IN METASTATIC-TUMOUR TISSUE OF HUMAN LIVERALHADEFF JA; HOLZINGER RT.1982; BIOCHEM. J. (LOND.); ISSN 0006-2936; GBR; DA. 1982; VOL. 201; NO 1; PP. 95-99; BIBL. 14 REF.Article

EXCRETION-REUPTAKE ROUTE OF BETA -HEXOSAMINIDASE IN NORMAL AND I-CELL DISEASE CULTURED FIBROBLASTSVLADUTIU GD; RATTAZZI MC.1979; J. CLIN. INVEST.; USA; DA. 1979; VOL. 63; NO 4; PP. 595-601; BIBL. 22 REF.Article

PURIFICATION AND SOME PROPERTIES OF BOVINE LIVER BETA -ACETYLHEXOSAMINIDASE.TANAKA M; KYOSAKA S; MURATA S et al.1978; CHEM. PHARM. BULL.; JPN; DA. 1978; VOL. 26; NO 4; PP. 1188-1194; BIBL. 16 REF.Article

BOVINE LIVER BETA -ACETYLHEXOSAMINIDASE. PURIFICATION BY HYDROPHOBIC AFFINITY CHROMATOGRAPHY AND HETEROGENEITYTANAKA M; KYOSAKA S; MURATA S et al.1978; CHEM. PHARM. BULL.; JPN; DA. 1978; VOL. 26; NO 10; PP. 3225-3228; BIBL. 12 REF.Article

EFFECT OF SURAMIN ON THE ACTIVITIES OF DEGRADATIVE ENZYMES OF SPHINGOLIPIDS IN RATSCONSTANTOPOULOS G; REES S; CRAGG BG et al.1981; RES. COMMUN. CHEM. PATHOL. PHARMACOL.; ISSN 0034-5164; USA; DA. 1981; VOL. 32; NO 1; PP. 87-97; BIBL. 8 REF.Article

LYSOSOMAL GLYCOSIDASE ACTIVITIES IN HUMAN HAIR ROOTS.PHILLIPS NC; THORPE R.1978; CLIN. CHIM. ACTA; PAYS-BAS; DA. 1978; VOL. 83; NO 1-2; PP. 93-98; BIBL. 13 REF.Article

SERUM BETA -HEXOSAMINIDASES IN PREGNANCYLOWDEN JA.1979; CLIN. CHIM. ACTA; NLD; DA. 1979; VOL. 93; NO 3; PP. 409-417; BIBL. 18 REF.Article

HUMAN PLACENTAL N-ACETYL-BETA -D-HEXOSAMINIDASE ISOZYMES. ACTIVITY TOWARD NATIVE HYALURONIC ACID.BACH G; GEIGER B.1978; ARCH. BIOCHEM. BIOPHYS.; USA; DA. 1978; VOL. 189; NO 1; PP. 37-43; BIBL. 31 REF.Article

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